[HN Gopher] An epigenetic editor to silence genes
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       An epigenetic editor to silence genes
        
       Author : Teever
       Score  : 120 points
       Date   : 2024-07-02 19:50 UTC (1 days ago)
        
 (HTM) web link (www.science.org)
 (TXT) w3m dump (www.science.org)
        
       | ProjectArcturis wrote:
       | Very impressive work. Just in mice so far but this looks very
       | promising for Huntington's in particular.
        
       | dluan wrote:
       | Eric and Sonia are incredible human beings hellbent on a mission.
       | Awe inspiring.
        
         | dluan wrote:
         | Here's a thread breaking down showing how it they managed to
         | get the viral transporter to self-regulate and "turn itself
         | off" after target gene silencing in the brain:
         | https://x.com/cureffi/status/1806404934658892013
         | 
         | And for further context, this work came out of the Weissman Lab
         | at MIT and a collaboration with a group called CureFFI. In
         | particular, there are two scientists there who have had an
         | utterly incredible story. I don't like it when VCs and such try
         | to attach onto someone else's shine, but seeing their story
         | develop and constantly push forward after getting a start on a
         | little website that I helped to create has been one of the most
         | awesome things in my life. For over 10 years they've been going
         | and going and going. The incredible sci-fi technical
         | achievements here aside, it's also just an amazing human story
         | of tenacity and curiosity. It's hard to talk about them without
         | getting emotional once you read their story.
         | 
         | Alzheimer's, Parkinson's, Huntington's, etc. Will be exciting
         | to see what's next.
         | 
         | https://www.newyorker.com/books/page-turner/a-prion-love-sto...
         | , https://www.nytimes.com/2020/07/07/health/rare-diseases.html
         | , https://experiment.com/projects/can-anle138b-delay-the-
         | onset...
        
           | knodi123 wrote:
           | > it's also just an amazing human story of tenacity and
           | curiosity. It's hard to talk about them without getting
           | emotional once you read their story.
           | 
           | In their own words:
           | 
           | https://www.cureffi.org/about/
        
       | flobosg wrote:
       | I was reminded of this comment exchange from last May:
       | https://news.ycombinator.com/item?id=40439379#40440171. TIL that,
       | according to this paper, antisense treatment in the brain has
       | some drawbacks:
       | 
       | > Treatment of mice with antisense oligonucleotides (ASOs)
       | targeting the _Prnp_ transcript decreases expression of PrP and
       | extends the survival of mice previously infected with misfolded
       | PrP (6); however, the limited efficacy of ASOs and the
       | requirement for chronic intrathecal dosing highlight the need for
       | a more potent therapy.
        
         | Zenzero wrote:
         | > requirement for chronic intrathecal dosing
         | 
         | Well that's a pretty wicked drawback if I've ever heard one.
        
       | hilbert42 wrote:
       | _" ...new epigenetic editor that can silence the expression of
       | prion protein (PrP) in the brains of mice and offers a fresh
       | approach to the treatment of neurodegenerative diseases."_
       | 
       | Wonderful news, let's hope it lives up to expectations.
        
       | teeray wrote:
       | I wonder if this could be used to neutralize HIV genes that have
       | been reverse transcribed in.
        
       | Kalanos wrote:
       | How fleeting are the modifications? How specific are they?
       | Wouldn't it makes more sense to deliver a gene that produces
       | RNAi?
        
       | A_D_E_P_T wrote:
       | Of course it's possible to use this sort of therapy to prevent
       | disease, by knocking out single genes associated with the
       | development of disease.
       | 
       | It's just as possible to silence single genes that, when
       | silenced, may elicit substantial positive effects in healthy
       | adults. Part of George Church's list, by no means comprehensive,
       | is:
       | 
       | MSTN -/- Lean muscle growth
       | 
       | SCN9A -/- Insensitivity to pain
       | 
       | ABCC11 -/- Low Odor production
       | 
       | CCR5, FUT2 -/- Virus resistance
       | 
       | PCSK9 -/- Low coronary disease
       | 
       | SLC30A8 -/+ Low T2 Diabetes
       | 
       | There are many others. Knocking out ACTN3, for instance, might
       | remodel skeletal muscle for better endurance performance, and
       | certain athletes don't express the gene.
        
         | dekhn wrote:
         | Sadly, that's not how most phenotypes work. While some
         | diseases/undesirable phenotypes are indeed simple mendelian,
         | and some diseases/undesireable phenotypes can be "fixed" by
         | knocking down a gene, in real life, gene therapy of any kind is
         | actually extremely complex, determined by the interaction of
         | many genes/gene products/regulatory regions/environment, with
         | non-linear combinatory effects.
         | 
         | Church has been selling some fairly naive ideas for some time,
         | and he knows better.
        
           | A_D_E_P_T wrote:
           | It's clearly how things work on rare occasion, which is self-
           | evidently obvious in MSTN knockout animals, and certain other
           | gene knockout phenotypes.
           | 
           | It's the exception rather than the rule, of course, as many
           | if not most traits -- like, most famously, height and IQ --
           | are polygenic and mediated by a network of many genes of
           | small effect.
           | 
           | There's still _a lot_ you can do by silencing certain
           | individual genes. I wouldn 't dismiss it out of hand.
        
             | dekhn wrote:
             | Even knockout phenotypes of single-trait genes can be
             | awfully complex (if your goal is to engineer a health
             | solution). I don't think than HN comments are a
             | particularly useful place to litigate the faults of genetic
             | thinking, but let me give an example from my own personal
             | experience:
             | 
             | When I was a postdoc at berkeley, my advisor gave me a
             | project to work on. A lab down the road at Stanford working
             | with yeast had done a series of knockouts, precisely
             | eliminating one gene at a time. They reported a number of
             | fatal knockouts in genes that previously had no known
             | function (or a non-necessary function), concluding that the
             | genes presumably had some sort of necessary function for
             | viability (such as housekeeping genes, but not in an
             | obviously necessary way).
             | 
             | Since I'm a DNA nerd I spent time looking at the nature of
             | the genes that were knocked out, and did a bunch of
             | analysis. First I categorized the genes in various ways and
             | didn't see any patterns. But, in the past I'd heard of
             | overlapping genes, and mostly for fun/edification, I taught
             | myself some CS I didn't know and created a data structure
             | and algorithm that allowed me to find all the pairs of
             | 'overlapping' genes
             | (https://www.nature.com/articles/s41576-021-00417-w) in the
             | yeast genome and found that for every single gene they had
             | newly identified as necessary, it overlapped an already
             | known housekeeping gene (overlapping genes were not, in the
             | early 2000s, widely appreciated).
             | 
             | I spoke to my advisor and told him that I reasoned that the
             | authors had made a mistake: in every case where they
             | identified the gene as being necessary, they had
             | accidentally disabled a housekeeping gene that was already
             | known to be necessary for viability, and incorrectly
             | concluded that the gene they knocked out intentionally was
             | the cause of loss of viability. I hope that makes sense-
             | it's basically a "false positive" that had another
             | explanation: they had knocked out two genes when they
             | thought they had knocked out one.
             | 
             | My advisor agreed and I sent my results to the authors, who
             | never responded. Their subsequent paper explicitly
             | mentioned my observations, without crediting me.
             | 
             | Since then, I've come to believe that much of what we
             | believe about genotypes and phenotypes, even in cases where
             | the outcome seems quite straightforward, linear, and
             | single-cause, is instead an error of preconcieved
             | assumptions. It greatly reduced my confidence in
             | geneticists (I'm a biophysicist- highly quantitative,
             | interested in the molecular cause-and-effect) ability to
             | make strong statements.
             | 
             | I don't work in this area any more (it's more lucrative to
             | move data for biologists than it is to be a biologist) but
             | I strongly suspect that I if enabled my OCD bit and spent
             | more than a month analyzing MSTN knockouts, I would find
             | that something which is "self-evidently obvious in MSTN
             | knockouts" is in fact much more complex and subtle than the
             | narrative in the literature.
        
           | WhitneyLand wrote:
           | >gene therapy of any kind is actually extremely complex
           | 
           | Yet there's people on YouTube self administering gene therapy
           | to cure lactose intolerance.
           | 
           | Not an endorsement, just to say it's interesting how easy
           | it's becoming to do these things.
        
       | the__alchemist wrote:
       | Does anyone have a linky? The usual route is not working, maybe
       | due to it being new.
        
       | woliveirajr wrote:
       | Remembers me this book:
       | https://www.goodreads.com/book/show/54120408-klara-and-the-s...
       | 
       | Although the main plot is about AI, the real reason why the
       | protagonist exists is very interesting about epigenetic...
        
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